Rotor's syndrome
Last reviewed 01/2018
Rotor's syndrome is an autosomal recessive condition characterised by a chronic, predominantly conjugated hyperbilirubinaemia. The mechanism is similar to that seen in the Dubin-Johnson syndrome, with defective excretion of organic anions into bile.
The liver is a normal colour on biopsy, unlike Dubin-Johnson syndrome.
The prognosis is excellent.