Dandy-Walker syndrome
Last reviewed 04/2022
Dandy-Walker Syndrome is a rare congenital abnormality in which there is usually an absence of the foramina of Magendie and Luschka.
It is characterised by:
- cystic dilatation of the fourth ventricle due usually to absence of the foramina
- dilatation of the third and lateral ventricles - but to a lesser extent than the fourth
- enlargement of the posterior fossa with a high tentorium cerebelli and transverse sinuses
- wide separation of the cerebellar hemispheres with a small vermis, displaced laterally
- various other developmental abnormalities in 65% of patients