haemophilia
Last reviewed 01/2018
These are a group of genetic disorders characterized by a deficiency of one of the coagulation pathway factors.
Haemophilia A is characterized by a deficiency of one subunit of factor VIII (factor VIII C).
Haemophilia B is the result of a deficiency of factor IX.
Von Willebrand's disease is a result of a variable deficiency of subunits of factor VIII (factor VIII RAG and factor VIII RiCoF) with a relatively normal factor VIII C level.
immediate treatment of bleeding
von Willebrand's disease (congenital deficiency of von Willebrand's factor )