differential diagnosis of ANCA associated vasculitis

Last reviewed 09/2022

Mimics of systemic vasculitis.

• 1. Systemic multisystem disease
  • Infection
    • Subacute bacterial endocarditis
    • Neisseria meningitidis
    • Rickettsiae
  • Malignancy
    • Metastatic carcinoma
    • Paraneoplastic
  • Other
    • Sweet syndrome
    • Connective tissue disorders
      
      
• 2. Vessel occlusion
  • Embolic
    • Cholesterol crystals
    • Atrial myxoma
    • Mycotic (infection)
  • Thrombotic
    • Antiphospholipid syndrome
    • Procoagulant states
    • Calciphylaxis
  • Other
    • Ergotism
    • Radiation
    • Degos syndrome
    • Severe Raynaud's phenomenon
    • Acute digital loss (atheromatous)
      
      
• 3. Angiographic appearances
  • Aneurysmal
    • Fibromuscular dysplasia
    • Neurofibromatosis
  • Occlusion
    • Coarctation of the aorta

     

Reference:

• 1) ARC Autumn 2012. Topical Reviews - ANCA-associated vasculitis; 1:1-12.