congenital ichthyosiform erythrodermas
Last reviewed 01/2018
- this is a group of rare inflammatory ichthyoses - this group is divided into nonbullous ichthyosiform erythroderma and lamellar ichthyosis
- the pathology of congenital ichthyosiform erythrodermas is confined to the skin; intellect and growth is normal; in general, there is little improvement with age